5 Facts you should know about

APDS

Imaging Findings: chest imaging modalities such as chest X-ray and CTs can show evidence of bronchiectasis, airway wall thickening, mucus plugging, and pulmonary nodules in APDS patients

Airway Clearance Therapy: APDS patients with chronic lung disease may benefit from airway clearance techniques, such as chest physiotherapy, positive expiratory pressure devices, and nebulized hypertonic saline

Genetic Testing: Patients that have recurrent pulmonary infections may have an underlying immune disorder, and should be referred for a genetic testing evaluation

Immunoglobulin Replacement Therapy (IVIG): IVIG is commonly used in APDS to provide passive immunity and reduce the frequency and severity of infections

Multidisciplinary Care: Management of APDS-related respiratory complications often requires collaboration with immunologists, infectious disease specialists, and respiratory therapists reveal obstructive or restrictive patterns in APDS patients, reflecting airway obstruction, bronchiolitis, or interstitial lung involvement

See our full disease profile

Rare Oncology News